RATIONALE
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,peds test - 75 topics
2
1. Idiopathic Thrombocytopenia Purpura
○ A hemorrhagic autoimmune disorder that causes excessive destruction of platelets
○ Symptoms → sometimes
NO symptoms
i. Purpura (easy/excessive bruising) & Petechiae ii.
Bleeding from gums/nose/mucus membranes iii.
Blood in urine or stool iv. Heavy menstrual flow
& low PLT count
○ Causes → immune system attacking its own platelets,
viral illness (flu/mumps)
○ Risk Factors → sulfa drugs, systemic lupus erythematosus, pregnancy,
, viruses
○ Diagnosis → CBC, blood smear, bone marrow exam (platelets are
produced in the bone marrow)
○ Labs → Platelets will be below 20,000. Normal range = 150,000-450,000
INR, PT & PTT high
○ Treatment → Acute ITP resolves spontaneously
within 6 months
i. Corticosteroids ii. Discontinuation of meds known to cause ITP
iii. Immunosuppressive agents & IV immune
globulin iv. Splenectomy & Chemotherapy
agents
○Nursing Considerations
i. Assess activities that increase risk for bleeding ii. Instruct client to avoid
aspirin & NSAID’s = high risk drugs for bleeding iii. Taking any sulfa-
based meds & any other PLT altering meds? iv. Avoid constipation &
using dental floss, use soft- bristled toothbrush
v.Instruct children about no contact sports, bike riding, skateboarding, climbing or running
vi. Encourage quiet activities vii. Inform HCP if there is head or abdomen trauma
○ Signs of Improvement → PLT count of
100,000- 400,000
→ A student nurse presents a conference on hematological disorders in children.
The student nurse identifies which information should be included.. presentation
about immune thrombocytopenia purpura (ITP)? Immune thrombocytopenia purpura
is caused by excessive destruction of platelets. There is discoloration due to petechiae, and
the bone marrow is normal.
2.Developmental Dysplasia of the Hip
● Definition → spectrum of conditions where there’s an abnormal relationship
between the proximal femur & acetabulum. There are 3 forms: dysplasia,
subluxation (mis-alignment of the vertebrae) & dislocation
●Signs & Symptoms
○ Asymmetrical skin folds (gluteal folds)
○Galeazzi sign (shortening of limb on affected side)
○Limited hip abduction & hip instability
○Lordosis (curvature of the lumbar and cervical regions of the human spine)
○Waddling gait
● Diagnostic Tests → Trendelenburg test (one leg up = opposite hip drops),
XRAY, MRI, US
● Treatment
○Pavlik harness (“overalls”), spica cast (legs) & surgical correction
●Nursing Care
, ○Reassure parents that early, prompt treatment will probably result in complete correction
3
○Encourage parent to stay with child during his/her first few days in cast/harness
○Spica Cast Treatment: keep cast dry & change child’s diapers often, turn Q2 &
Q4 at night, check color, sensation & motion of child’s legs & feet
○Give Benadryl if child complains of itching or cool blow dryer - Do NOT scratch with objects
○Encourage parents to let child sit at a table, floor & play with other kids (socialize)
○Watch for signs that the child is outgrowing the cast - cyanosis
→ The nurse cares for the 2-week-old infant diagnosed with developmental dysplasia
of the hip (DDH). The nurse notes which finding is consistent diagnosis of DDH?
Asymmetry of the gluteal folds.
3. Osteogenesis Imperfecta (Brittle Bone Disease) → inherited syndrome causing
fractures & bone deformities, most common osteoporosis syndrome in children
→ bones become brittle
●Signs & Symptoms
○Multiple fractures at birth & during childhood causing limb & spinal deformities
○Mosaic pattern to the bones (puzzle like pieces)
○Blue sclera of the eye
○Dental deformities
○Progressive hearing loss
● Treatment → NONE KNOWN, just focus on preventing &
treating fractures
○Prenatal US to detect disease in utero
○Growth hormone to stimulate bone growth
○Calcitonin to aid in bone healing
○Bisphosphonates to increase bone mass
○Surgery to correct fractures & place rods to correct deformities
○Physical Therapy & moderate exercise to increase bone density
● Nursing Care → provide a safe, protective environment to
minimize any trauma
○Educate parents on how to help kids live a productive, safe life
○Raise side rails up on cribs & beds to reduce falls
○Remove objects on the floor that could cause tripping
○ Lifting children with care → What special instruction
should you give to the parents? Reposition the child carefully
4. Meningitis → inflammation of the meninges due to either a
virus or bacteria