User Howard Kinlock
Course 202030 Summer 2020 BCHM 551-B01 LUO
Test Quiz 4
Started 6/7/20 10:03 AM
Submitted 6/7/20 1:13 PM
Due Date 6/7/20 11:59 PM
Status Needs Grading
Attempt Score 0 out of 60 points
Time Elapsed 3 hours, 9 minutes out of 1 hour OVER TIME
Instructions
Time limit: 30 minutes
30 multiple-choice questions
Open-book/open-notes
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Results Displayed Submitted Answers, Feedback
Question 1 0 out of 2 points
Human adipose tissues respond to all except?
Selected Answer: Cortisol
Question 2 2 out of 2 points
A 22 year old Biology major from Quebec, Canada has been experiencing progressive muscle weakness,
loss of vision in both eyes with a cherry red spot found on examination of his retina and most recently has
been experiencing a decline in his mental faculties. There was no hepatomegaly or splenomegaly and no
abnormal hematological findings. His fibroblasts showed elevated levels of gangliosides. You will suspect
that the patient is most likely deficient in;
Selected Answer: Hexosaminidase A
Question 3 2 out of 2 points
In a patient with a defect in the gene that codes for the protein – N-acetylglucosamine-1-phosphodiester-N-
acetylglucosaminidase will likely exhibit which of these biochemical features;
Selected Answer: All of these
Question 4 2 out of 2 points
Unlike I-cell disease, this lysosomal enzyme activity is either diminished or not detectable in Pseudo-Hurler
Polydystrophy;
Selected Answer: Arylsufatase A
Question 5 2 out of 2 points
What amino acid combines with palmitoyl CoA to form sphingosine?
Selected Answer: Serine
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Question 6 2 out of 2 points
A patient with Niemann-Pick disease will show an increase in intracellular accumulation of_________?
Selected Answer: Sphingomyelin
Question 7 2 out of 2 points
This condition results from excessive accumulation of globotriaosyceramide and affects males only causing
skin rashes and potentially renal failure;
Selected Answer: Fabry’s disease
Question 8 2 out of 2 points
In an alcoholic patient who has not eaten food for the past three days, which of these factors will likely
contribute to an elevation in plasma ketone bodies;
Selected Answer: All of these
Question 9 2 out of 2 points
Niemann-Pick disease is a type of lipid storage disease caused by the genetic deficiency of ___?
Selected Answer: Sphingomyelinase
Question 10 2 out of 2 points
The intracellular activity levels of these enzymes will be significantly diminished in a patient with I-cell
disease except___________?
Selected Answer: Acid phosphatase
Question 11 0 out of 2 points
A 40 year old man with a history of bleeding and pancytopenia now presents with leg pain. CT scan reveals
a thinning of the right femoral head and a bone marrow biopsy reveals Gaucher’s disease. Which material
will be found to be accumulating abnormally in his lysosomes?
Selected Answer: Gangloside
Question 12 0 out of 2 points
Hepatocytes are unable to convert ketones to acetyl CoA for energy production because they
lack_________?
Selected Answer: HMG CoA reductase
Question 13 2 out of 2 points
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