Maple syrup urine disease Study guides, Class notes & Summaries

Spectrophotometer correct answer: Measures concentration in a solution by calculating absorbance from the transmitted light Beer's law correct answer: Concentration of a substance is directly proportional to absorbed light or inversely proportional to the logarithm of transmitted light Fluorescence or fluorometry correct answer: The emited light of some substances is at a longer wavelength than the absorbed light Turbidimetry correct answer: Method that measures the scattered light...

Functional Medicine Final Exam Questions With 100% Correct Solutions Latest 2024/2025. What are the primary organic acid abnormalities that occur in carnitine deficiency? correct answers -adipate -suberate -ethylmalonate What patterns of abnormalities discriminate mitochondrial inefficiency from ammonia challenge as a cause of citric acid elevation? correct answers -high citrate, aconitate, isocitrate + orotate indicates ammonia challenges -wihtout orotate= mitochondrial inefficiency Wha...

Which of the following aminoacidopathies is NOT caused by an enzyme deficiency? Choose one answer. a. phenylketonuria b. alkaptonuria c. maple syrup disease d. cystinuria d. cystinuria What method is most commonly used to measure total protein? Choose one answer. a. dye binding b. Kjeldahl c. Biuret d. refractometry c. Biuret Which of the following is the preferred reagent for measuring albumin by the dye binding method because there is less interfering substances? Cho...

NNP BOARDS EXAM REVIEW QUESTIONS AND ANSWERS, GRADED A+/ Intralobar sequestration associated with Morgagni hernia Most common congenital viral infection CMV Subarachnoid hemorrhage seizure presentation Soon after birth Candidal infection hallmarks Hyperglycemia + thrombocytopenia Deficiency of Branched-chain alpha-ketoacid dehydrogenase/increased valine, isoleucine, leucine Maple Syrup Urine disease Clubfoot findings Forefoot varus, heel varus, ankle equines Clubfoot is associated ...

40y/o Male has a random glucose of 470. Lab finding is consistent with what disorder? Diabetes Mellitus Highly alkaline buffered urine can cause what error on a urine dipstick? false positive protein In the urine dipstick test for protein, to which protein is the test more sensitive? Albumin or globulin? Albumin Ceruloplasmin, follicle stimulating hormone (FSH), and fibrinogen are all what? Glycoproteins Diabetic acidosis, renal failure and prolonged vomiting can ...

MT AAB Chemistry Which of the four elements in proteins differentiated this class of substances from carbohydrates and lipids? - ANSWER Nitrogen Which of the proteins is soluble in water? - ANSWER Albumin How are amino acids joined together to form a chainlike structure? - ANSWER Peptide bonding Proteins may become denatured when subjected to mechanical agitation, heat, or chemical treatment. What does denaturation of proteins refer to? - ANSWER Alteration of tertiary structure Whic...

IBCLC Exam Flashcards UPDATED 2023 Micrognathia Condition where jaw is undersized; common but can interfere with feeding and breathing PKU (phenylketonuria) Body does not produce enzyme to break-down amino acid phenylalanine and this builds-ups in blood; need low phe formula and CAN breastfeed Maple Syrup Disease Body is unable to break-down certain proteins/amino acids (leucine); sweet smelling urine. Need low protein diet/special formula i.e. Ketonex-1. BF CONTRAINDICATED Gal...

National Council Licensure Examination(NCLEX-RN) VERSION V12.35 Verified Questions and Answers for 2022/2023 Exam : NCLEX-RN Title : National Council Licensure Examination(NCLEX-RN) Vendor : NCLEX Version : V12.35 NO.1 A depressed client is seen at the mental health center for follow-up after an attempted suicide 1 week ago. She has taken phenelzine sulfate (Nardil), a monoamine oxidase (MAO) inhibitor, for 7 straight days. She states that she is not feeling any better....

AAB MT Chemistry- Practice Questions and Answers 100% Pass Which of the following aminoacidopathies is NOT caused by an enzyme deficiency? Choose one answer. a. phenylketonuria b. alkaptonuria c. maple syrup disease d. cystinuria - CORRECT ANSWER-d. cystinuria What method is most commonly used to measure total protein? Choose one answer. a. dye binding b. Kjeldahl c. Biuret d. refractometry - CORRECT ANSWER-c. Biuret Which of the following is the preferred reagen...

ATI Nutrition Practice Test A & B 1. A nurse is caring for a client who expresses a desire to lose weight. Which of the following actions should the nurse take first? a. Recommend checking weight once weekly. b. Obtain a 24-hr dietary recall. c. Assist with creating an exercise plan. d. Initiate a plan for diet modification. 2. A nurse is teaching about nutritional requirements for a client who is starting a vegetarian diet. Which of the following information should the nurse include in...