PNCB Knowledge test Exam Toolkit Questions
and Verified Marking Scheme 2023/2024
What deficiency results in acrodermatitis enteropathy - correct
answer zinc
What deficiency presents with perioral and acral dermatitis,
diarrhea and alopecia - correct answer zinc
What vitamin deficiency results in megaloblastic anemia -
correct answer b12
What deficiency presents as muscle weakness, tremors and
paresthesia - correct answer magnesium
What vitamin should children with williams syndrome not be
given - correct answer vitamin d
What syndrome presents with supravalvular aortic stenosis,
periorbital fullness, blue irides with a stellate pattern, full lips
and a hoarse voice - correct answer williams syndrome
Qhat are the 3 most common causes of microcephaly - correct
answer infection, trauma, and hypoxic ischemic insult
What is the most common form of child matreatment in the us -
correct answer neglect
,Which syndrome is at an increased risk of developing breast
cancer - correct answer klinefelter syndrome
When can a child make a tower of 3 and make a line - correct
answer 15 months
When can a child make a tower of 4, scribble and make a vertical
line - correct answer 18 months
When can a child milke a tower of 9 cubs, draw a vertical and
horizontal lines, and imitate a circular stroke - correct answer
30 months
Which deficiency presents with diffuse weakness, cerebellar
ataxia and partial ophthalmoplegia - correct answer vitamin e
Which deficiency presents with irritability and exaggered startle
response and seiures - correct answer vitamin b 6
Which deficiency manifests as proximal weakness, waddling gait
- correct answer vitamin d
What heart condition has a widended pulse pressure, continuous
machine like murmur - correct answer pda
Which murmur presents with a soft systolic ejection murmur,
fixed spilting s2 - correct answer asd
,Which murmur usually presents with a pansystolic murmur -
correct answer vsd
What is associated with a systolic ejection murmur and radiated
to the neck - correct answer aortic stenosis
What time of inherited deficiecny is pdh - correct answer x
linked or autosomal recessive
What is used in accidental pediatric benzodiazepine poisioning -
correct answer flumazenil
What is it when there is a splitting of the spinal cord in two
portions by the midline septum - correct answer
diastematomyelia
What is it when there is an isolated protrusion of the meninges
into a bony defect within the vertebral column, generally covered
by skin and not associated with neurologic deficits - correct
answer meningocele
What is it when there is a protrusion of potentiall all layers of the
intraspinal contents through a bony defect generally in the
lumbosacral region - correct answer myelomeningocele
What is it when there is the presence of two central canals that
are each surrpunded by gray and white matter as in a normal
spinal cord - correct answer diplomyelia
, What is the most common cause of atraumatic sudden death in
young athlets - correct answer hypertrophic cardiomyopathy
What is the most common heart defect in down syndrome kids -
correct answer atrioventricular septal defect
What is common in the setting of digoxin overdose - correct
answer hyperkalemia
How do you treat hyperkalemia in the setting of digoxin overdose
- correct answer iv digibind (fab) adminstration
What should you never given with digoin toxicitiy due to the risk
of sudden cardaic death - correct answer calcium
What is the most common cause of gastroenteritits when
consuming eggs or mayo - correct answer staphylococcus
aureus
Unilateral uveal coloboma involving the iris is concerning for
which syndrome - correct answer charge
What is the most common cause of congenital deaf blindness -
correct answer charge syndrome
Why should atypical neuroleptic be tapered slowly - correct
answer prevent withdrawl akathisias
and Verified Marking Scheme 2023/2024
What deficiency results in acrodermatitis enteropathy - correct
answer zinc
What deficiency presents with perioral and acral dermatitis,
diarrhea and alopecia - correct answer zinc
What vitamin deficiency results in megaloblastic anemia -
correct answer b12
What deficiency presents as muscle weakness, tremors and
paresthesia - correct answer magnesium
What vitamin should children with williams syndrome not be
given - correct answer vitamin d
What syndrome presents with supravalvular aortic stenosis,
periorbital fullness, blue irides with a stellate pattern, full lips
and a hoarse voice - correct answer williams syndrome
Qhat are the 3 most common causes of microcephaly - correct
answer infection, trauma, and hypoxic ischemic insult
What is the most common form of child matreatment in the us -
correct answer neglect
,Which syndrome is at an increased risk of developing breast
cancer - correct answer klinefelter syndrome
When can a child make a tower of 3 and make a line - correct
answer 15 months
When can a child make a tower of 4, scribble and make a vertical
line - correct answer 18 months
When can a child milke a tower of 9 cubs, draw a vertical and
horizontal lines, and imitate a circular stroke - correct answer
30 months
Which deficiency presents with diffuse weakness, cerebellar
ataxia and partial ophthalmoplegia - correct answer vitamin e
Which deficiency presents with irritability and exaggered startle
response and seiures - correct answer vitamin b 6
Which deficiency manifests as proximal weakness, waddling gait
- correct answer vitamin d
What heart condition has a widended pulse pressure, continuous
machine like murmur - correct answer pda
Which murmur presents with a soft systolic ejection murmur,
fixed spilting s2 - correct answer asd
,Which murmur usually presents with a pansystolic murmur -
correct answer vsd
What is associated with a systolic ejection murmur and radiated
to the neck - correct answer aortic stenosis
What time of inherited deficiecny is pdh - correct answer x
linked or autosomal recessive
What is used in accidental pediatric benzodiazepine poisioning -
correct answer flumazenil
What is it when there is a splitting of the spinal cord in two
portions by the midline septum - correct answer
diastematomyelia
What is it when there is an isolated protrusion of the meninges
into a bony defect within the vertebral column, generally covered
by skin and not associated with neurologic deficits - correct
answer meningocele
What is it when there is a protrusion of potentiall all layers of the
intraspinal contents through a bony defect generally in the
lumbosacral region - correct answer myelomeningocele
What is it when there is the presence of two central canals that
are each surrpunded by gray and white matter as in a normal
spinal cord - correct answer diplomyelia
, What is the most common cause of atraumatic sudden death in
young athlets - correct answer hypertrophic cardiomyopathy
What is the most common heart defect in down syndrome kids -
correct answer atrioventricular septal defect
What is common in the setting of digoxin overdose - correct
answer hyperkalemia
How do you treat hyperkalemia in the setting of digoxin overdose
- correct answer iv digibind (fab) adminstration
What should you never given with digoin toxicitiy due to the risk
of sudden cardaic death - correct answer calcium
What is the most common cause of gastroenteritits when
consuming eggs or mayo - correct answer staphylococcus
aureus
Unilateral uveal coloboma involving the iris is concerning for
which syndrome - correct answer charge
What is the most common cause of congenital deaf blindness -
correct answer charge syndrome
Why should atypical neuroleptic be tapered slowly - correct
answer prevent withdrawl akathisias
